Recommendations regarding splenectomy in hereditary hemolytic anemias
Subnetwork: Bone marrow failure, Red blood cell defects
Disease group/s: Alpha- thalassaemia disorders, Beta- thalassaemia disorders, Congenital dyserythropoietic anemia (CDA), Hereditary Elliptocytosis, Hereditary Spherocytosis, Hereditary Stomatocytosis, Pyruvate Kinase Deficiency, Red blood cell enzyme defects, Sickle cell disorders
Scope and Purpose: 3. Treatment
Patients' involvement?: No
Rigour of development: A - Evidence and consensus based