ERN-EuroBloodNet, the ERN on Rare Hematological Diseases (RHDs)
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In this section you will find the list of Clinical Practice Guidelines (CPGs) and other Clinical Decision Making Tools (CDMTs) compiled and classified on Quality Domains. Please go to Guidelines and other CDMTs Section to see the methodology followed.

*Please note that classification for CPGs and other CDMTs on Bleeding and Coagulation disorders and Lymphoid malignances on Quality Domains is ongoing. Documents will be searchable soon.

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Recommendations regarding splenectomy in hereditary hemolytic anemias

Subnetwork: Bone marrow failure, Red blood cell defects

Disease group/s: Alpha- thalassaemia diseases, Beta-thalassemia and related diseases, Congenital dyserythropoietic anemia, Hereditary elliptocytosis, Hereditary spherocytosis, Hereditary stomatocytosis, Rare constitutional hemolytic anemia due to pyruvate kinase deficiency, Rare constitutional hemolytic anemia due to an enzyme disorder (Other than PKD), Sickle cell disease and related diseases

Scope and Purpose: 3. Treatment

Patients' involvement?: No

Rigour of development: A - Evidence and consensus based

Link: https://www.ncbi.nlm.nih.gov/pubmed/28550188

Guidelines for the diagnosis and management of adult aplastic anaemia

Subnetwork: Bone marrow failure

Disease group/s: Rare acquired aplastic anemia (Other than PNH), Blackfan-Diamond anemia, Rare constitutional aplastic anemia (Other than BDA, DKC, FA, SDS), Dyskeratosis congenita and related disorders, Fanconi anemia, Paroxysmal nocturnal hemoglobinuria, Shwachman-Diamond syndrome

Scope and Purpose: 5. Diagnosis and treatment

Patients' involvement?: No

Rigour of development: B - Consensus based

Link: https://www.ncbi.nlm.nih.gov/pubmed/26568159

Recommendations on hematopoietic stem cell transplantation for inherited bone marrow failure syndromes

Subnetwork: Bone marrow failure

Disease group/s: Rare acquired aplastic anemia (Other than PNH), Blackfan-Diamond anemia, Rare constitutional aplastic anemia (Other than BDA, DKC, FA, SDS), Dyskeratosis congenita and related disorders, Fanconi anemia, Paroxysmal nocturnal hemoglobinuria, Shwachman-Diamond syndrome

Scope and Purpose: 3. Treatment

Patients' involvement?: No

Rigour of development: B - Consensus based

Link: https://www.ncbi.nlm.nih.gov/pubmed/26052913

Transplantation for bone marrow failure: current issues

Subnetwork: Bone marrow failure

Disease group/s: Rare acquired aplastic anemia (Other than PNH), Blackfan-Diamond anemia, Rare constitutional aplastic anemia (Other than BDA, DKC, FA, SDS), Dyskeratosis congenita and related disorders, Fanconi anemia, Paroxysmal nocturnal hemoglobinuria, Shwachman-Diamond syndrome

Scope and Purpose: 3. Treatment

Patients' involvement?: No

Rigour of development: C - Expert opinion

Link: https://www.ncbi.nlm.nih.gov/pubmed/27913467

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